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中华胸部外科电子杂志 ›› 2023, Vol. 10 ›› Issue (03) : 183 -187. doi: 10.3877/cma.j.issn.2095-8773.2023.03.09

病例报告

纵隔单中心型Castleman病诊治体会及文献复习
王新桥(), 马超英, 张旭光   
  1. 032200 汾阳,山西医科大学附属汾阳医院心胸外科
  • 收稿日期:2022-11-22 修回日期:2023-04-26 接受日期:2023-05-16 出版日期:2023-08-28
  • 通信作者: 王新桥

Diagnosis and treatment of Castleman disease of mediastinal monocentric type and literature review

Xinqiao Wang(), Chaoying Ma, Xuguang Zhang   

  • Received:2022-11-22 Revised:2023-04-26 Accepted:2023-05-16 Published:2023-08-28
  • Corresponding author: Xinqiao Wang
引用本文:

王新桥, 马超英, 张旭光. 纵隔单中心型Castleman病诊治体会及文献复习[J]. 中华胸部外科电子杂志, 2023, 10(03): 183-187.

Xinqiao Wang, Chaoying Ma, Xuguang Zhang. Diagnosis and treatment of Castleman disease of mediastinal monocentric type and literature review[J]. Chinese Journal of Thoracic Surgery(Electronic Edition), 2023, 10(03): 183-187.

Castleman病是一种原因不明的淋巴组织增殖性疾病,发病率较低,又称巨大淋巴结细胞增生症、血管滤泡性淋巴组织增生,或血管瘤性淋巴错构瘤[1]。1956年首先由Castleman在一系列病例中描述[2]。Castleman病约70%见于胸腔,颈部占15%,腹部和骨盆占15%[3]。本病易误诊,现总结山西省汾阳医院分别于2021年3月及2022年7月收治的2例纵隔Castleman病患者病例资料,结合文献对其进行分析,以提高对该病的诊治水平。

图1 病例1胸部增强CT扫描提示左肺上叶纵隔旁见软组织肿块影伴钙化,大小约5.5 cm×3.9 cm
图2 病例1(A)及病例2(B)的手术大体标本
图3 病例1术后病理提示血管滤泡性淋巴组织增生
图4 病例2 胸部增强CT扫描提示前中纵隔偏左侧见类圆形软组织肿块,大小约6.5 cm × 3.3 cm,边缘光滑,内伴点状钙化
图5 病例2术后病理提示血管滤泡性淋巴组织增生
1
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[1] 丁政, 李向楠, 赵佳, 朱登彦, 吴恺, 赵松. 胸内巨大淋巴结增生症的外科诊疗分析[J]. 中华胸部外科电子杂志, 2015, 02(04): 254-258.
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